Concept information
PREFERRED TERM
void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 1997-03-11T00:00:00Z
skos:notation: 16735
DEFINITION
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Enzim bozukluğuna ilgili olarak gangliyositlerin dokularda birikmesi, gelişme geriliği, baş ve bacak titremeleri, körlük, felç, gliozis, miyelin ve nöron kayıplarıyla belirgin bir grup kalıtsal lipit depo hastalığı.
(tr)
Source: https://sozluk.gov.tr/
Created: 4/25/23
BROADER CONCEPT
- Sphingolipidose (de)
IN OTHER LANGUAGES
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داء العقد
Created: 2022-03-17T12:03:42Z
skos:notation: 16735
Arabic
-
神经节苷脂贮积病
Created: 2021-08-27T15:24:42Z
skos:notation: 16735
Chinese
-
神经节苷脂沉积症
Created: 2002-12-12T00:00:00Z
Last modified: 2021-08-27T15:24:42Z
skos:notation: 16735
-
gangliosidóza
Created: 2003-03-27T00:00:00Z
skos:notation: 16735
Czech
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gangliosidosis
Created: 1986-08-28T00:00:00Z
skos:notation: 16735
English
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gangliosidose
Created: 1987-04-01T00:00:00Z
Last modified: 2021-05-24T17:34:42Z
skos:notation: 16735
French
-
गैंगलिओसाईडोसिस
Created: 1986-08-28T00:00:00Z
skos:notation: 16735
Hindi
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gangliosidosis
Created: 1986-08-28T00:00:00Z
skos:notation: 16735
Hungarian
-
Gangliosidosi
Created: 2006-10-27T00:00:00Z
skos:notation: 16735
Italian
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ガングリオシド症、スフィンゴ脂質蓄積症、ガングリオシド蓄積症
Created: 2005-08-09T00:00:00Z
skos:notation: 16735
Japanese
-
갱그리오시도증
Created: 2009-12-02T00:00:00Z
skos:notation: 16735
Korean
-
گانگليوزيدوز
Created: 2007-04-20T00:00:00Z
skos:notation: 16735
Persian
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Gangliozydoza
Created: 2006-12-19T00:00:00Z
skos:notation: 16735
Polish
-
gangliosidose
Created: 1987-04-01T00:00:00Z
Last modified: 2021-05-24T17:34:42Z
skos:notation: 16735
Portuguese
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gangliozidoză
Created: 2022-02-15T13:27:04
skos:notation: 16735
Romanian
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ганглиозидоз
Created: 2009-04-20T00:00:00Z
skos:notation: 16735
Russian
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gangliozidóza
Created: 2005-12-16T00:00:00Z
skos:notation: 16735
Slovak
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Gangliosidosis
Created: 1990-06-18T00:00:00Z
skos:notation: 16735
Spanish
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gangliosidosis
Created: 1986-08-28T00:00:00Z
skos:notation: 16735
Swahili
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gangliyosidozis
Created: 2011-11-20T20:44:02Z
Last modified: 2013-08-27T20:08:53Z
skos:notation: 16735
Turkish